Abstract
Management of chronic thromboembolic pulmonary hypertension: current status and emerging options
Author(s): Aravinda Page, Jason M Ali, Jane Maraka, Robert Mackenzie-Ross, David P Jenkins Chronic thromboembolic pulmonary hypertension (CTEPH) is the only cause
of pulmonary hypertension for which there is a potential cure, in the form of surgical pulmonary
endarterectomy. There is a strong link between pulmonary embolism and the development
of CTEPH. Although initially felt to be a rare complication, this position has been reviewed,
following several studies suggesting that up to 8.8% of patients develop CTEPH within the
2 years following pulmonary embolism. However, there is a significant discrepancy in the
number of patients being diagnosed, referred and treated for CTEPH. In this review, we
discuss the challenges of diagnosing CTEPH and present the current and emerging medical
and surgical management options available for patients suffering with CTEPH.